Diagnosis and treatment of supravalvular aortic stenosis and Wil

Chemistry: molecular biology and microbiology – Measuring or testing process involving enzymes or... – Involving nucleic acid

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435 911, 435 912, 536 231, 536 235, 536 2431, 536 2433, 935 1, 935 8, 935 77, 935 78, C12Q 168, C12P 1934, C07H 2102, C12N 1500

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058404899

ABSTRACT:
The invention relates to the identification of the molecular basis of supravalvular aortic stenosis (SVAS) and Williams syndrome. More specifically, the invention has identified that elastin causes or is involved in the pathogenesis of SVAS and Williams syndrome. Molecular variants of the elastin gene contribute to SVAS and Williams syndrome. The analysis of the elastin gene will provide an early diagnosis of subjects with SVAS and Williams syndrome. The diagnostic method comprises analyzing the DNA sequence of the elastin gene of an individual to be tested and comparing it with the DNA sequence of the native, non-variant elastin gene. In a second embodiment, the elastin gene of an individual to be tested is screened for mutations associated with SVAS or Williams syndrome. Presymptomatic diagnosis of SVAS and Williams syndrome will enable practitioners to prevent vascular obstruction using existing medical therapies like beta adrenergic blocking agents.

REFERENCES:
Ewart et al., "A human vascular disorder, supravalvular aortic stenosis, maps to chromosome 7," Proceedings of the National Academy of Sciences, Use, vol. 90, pp. 3226-3230, Apr. 1993.
Uittco et al., "Molecular biology and pathology of human elastin," Biomedical Society Transactions, vol. 19, pp. 824-829, 1991.
Fazio et al., "Human Elastin Gene: New Evidence for Localization of the Long Arm of Chromosome 7," American Journal of Genetics, 48:696-703, 1991.
Fazio e tal., "Cloning of Full-length Elastin cDNAs from a Human Skin Fibroblast Recombinant cDNA Library: Further Elucidation of Alternative Splicing Utilizing Exon-specific Oligonucleotides," The Jpurnal of Investigative Dermatology, vol. 91, No. 5, pa, Nov. 1988.
Uitto et al., "Molecular biology and pathology of human elastin," Biochemical Society Transactions, vol. 19, pp. 824-829, 1991.
Indik, Z. et al. (1987). "Alternative splicing of human elastin mRNA indicated by sequence analysis of cloned genomic and complementary DNA," Proc. Natl. Acad. Sci. USA 84:5680-5684.
Indik, Z. et al. (1987). "Structure of the 3' Region of the Human Elastin Gene: Great Abundance of Alu Repetitive Sequences and Few Coding Sequences," Connective Tissue Research 16:197-211.
O'Connor, W. et al. (1985). "Supravalvular Aortic Stenosis," Arch. Pathol. Lab. Med. 109:179-185.
Perou, M. (1961). "Congenital Supravalvular Aortic Stenosis," Arch. Pathol. 71:113-126.
Rosenbloom, J. et al. (1991). "Elastin Genes and Regulation of Their Expressions," Critical Reviews in Eukaryotic Gene Expression 1:145-156.
Sandberg, L. et al. (1981). "Elastin structure, biosynthesis, and relation to disease states," N. Engl. J. Med. 304:566-579.
Tromp, G. et al. (1991). "A to G polymorphism in ELN gene," Nucl. Acids Res. 19:4314.
Uitto, J. et al. (1991). "Molecular biology and pathology of human elastin," Biochem. Soc. Trans. 19:824-829.
Yeh, H. et al. (1987). "Sequence variation of bovine elastin mRNA due to alternative splicing," Coll. Relat. Res. 7:235-247.
Yoon, K. et al. (1985). "Analysis of the 3' region of the sheep elastin gene," Arch. Biochem. Biophys. 241:684-691.
Bashir, M.M. et al. (1989). "Characterization of the Complete Human Elastin Gene," J. Biol. Chem. 264:8887-8891.
Curran, M.E. et al. (1993). "The Elastin Gene Is Disrupted by a Translocation Associated with Supravalvular Aortic Stenosis," Cell 73:159-168.
Ewart, A.K. et al. (1993). "A human vascular disorder, supravalvular aortic stenosis, maps to chromosome 7," Proc. Natl. Acad. Sci. USA 90:3226-3230.
Fazio, M.J. et al. (1991) "Human Elastin Gene: New Evidence for Localization to the Long Arm of Chromosome 7," Am. J. Hum. Genet. 48:696-703.
Fazio, M.J. et al. (1988). "Cloning of Full-length Elastin cDNAs from a Human Skin Fibroblast Recombinant cDNA Library: Further Elucidation of Alternative Splicing Utilizing Exon-specific Oligonucleotides," J. Investigative Dermatology 91:458-464.
O'Connor et al., "Supravalvular Aortic Stenosis," Arch Pathol Lab Med, vol. 109, pp. 179-185, Feb. 1985.
Bashir et al., "Characterization of the Complete Human Elastin Gene," The Journal of Biological Chemistry, vol. 264, No. 15, pp. 8887-8891, May 25, 1989.
Sandberg et al., "Elastin Structure, Biosynthesis, and Relation to Disease States," The New England Journal of Medicine, vol. 304, No. 10, pp. 566-579, Mar. 5, 1981.

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